{"id":342,"date":"2014-03-27T15:16:53","date_gmt":"2014-03-27T14:16:53","guid":{"rendered":"http:\/\/s519078666.onlinehome.fr\/?page_id=342"},"modified":"2015-02-19T10:47:15","modified_gmt":"2015-02-19T09:47:15","slug":"maladie-rare","status":"publish","type":"page","link":"http:\/\/www.stargardt.fr\/test\/nos-missions\/maladie-rare\/","title":{"rendered":"Maladie rare"},"content":{"rendered":"<h2>Dystrophie maculaire h\u00e9r\u00e9ditaire la plus fr\u00e9quente<\/h2>\n<p><strong>La maladie de Stargardt est une maladie rare\u00a0d&rsquo;origine\u00a0g\u00e9n\u00e9tique. Elle repr\u00e9sente la dystrophie maculaire h\u00e9r\u00e9ditaire la plus fr\u00e9quente.<\/strong><\/p>\n<p>Une maladie est dite rare quand elle touche moins d\u2019une personne sur 2\u00a0000, soit pour la France moins de 30 000 personnes pour une maladie.<\/p>\n<p>Elle concerne 1,2 personne pour 10\u00a0000.<\/p>\n<table>\n<thead>\n<tr>\n<th>Pays<\/th>\n<th>Population totale<\/th>\n<th>ABCA4 1,2 \/10 000 personnes<\/th>\n<\/tr>\n<\/thead>\n<tbody>\n<tr>\n<td>AFRIQUE<\/td>\n<td>1 095 480 000<\/td>\n<td>131 458<\/td>\n<\/tr>\n<tr>\n<td>AM\u00c9RIQUE LATINE ET CARA\u00cfBES<\/td>\n<td>609 618 000<\/td>\n<td>73 154<\/td>\n<\/tr>\n<tr>\n<td>AM\u00c9RIQUE SEPTENTRIONALE<\/td>\n<td>353 430 000<\/td>\n<td>42 412<\/td>\n<\/tr>\n<tr>\n<td>ASIE<\/td>\n<td>4 292 880 000<\/td>\n<td>515 146<\/td>\n<\/tr>\n<tr>\n<td><b>EUROPE<\/b><\/td>\n<td><b>740 455 000 <\/b><\/td>\n<td><b>88 855 <\/b><\/td>\n<\/tr>\n<tr>\n<td>OC\u00c9ANIE<\/td>\n<td>38 228 400<\/td>\n<td>4 587<\/td>\n<\/tr>\n<tr>\n<td><strong>MONDE<\/strong><\/td>\n<td><strong>7 130 100 000<\/strong><\/td>\n<td><b>855 611 <\/b><\/td>\n<\/tr>\n<tr>\n<td>FRANCE<\/td>\n<td>63 000 000<\/td>\n<td>7 560<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<p><em>Source : Institut national d&rsquo;\u00e9tudes d\u00e9mographiques &#8211; <a href=\"http:\/\/www.ined.fr\/fr\/pop_chiffres\/pays_du_monde\/\" target=\"_blank\">www.ined.fr<\/a><\/em><br \/>\n<em>World Population Prospects. Nations Unies. 2011<\/em><\/p>\n<p>La forme la plus courante de cette dystrophie maculaire h\u00e9r\u00e9ditaire appara\u00eet avant l\u2019\u00e2ge de 20 ans (forme typique de l\u2019enfant). Elle touche les deux sexes et ne d\u00e9pend <em>a priori<\/em> d\u2019aucun facteur g\u00e9ographique.<\/p>\n<p>Il s&rsquo;agit d&rsquo;une maladie d&rsquo;\u00e9volution progressive avec perte de l&rsquo;acuit\u00e9 visuelle jusqu&rsquo;\u00e0 atteinte de valeurs basses. Les personnes atteintes de la maladie de Stargardt conservent la vision p\u00e9riph\u00e9rique et ne deviennent pas aveugles.<\/p>\n<p>Cette maladie rare n&rsquo;a pas d&rsquo;impact sur l&rsquo;esp\u00e9rance de vie.<\/p>\n<div style=\"padding-bottom:20px; padding-top:10px;\" class=\"hupso-share-buttons\"><!-- Hupso Share Buttons - https:\/\/www.hupso.com\/share\/ --><a class=\"hupso_toolbar\" href=\"https:\/\/www.hupso.com\/share\/\"><img src=\"http:\/\/static.hupso.com\/share\/buttons\/lang\/fr\/share.png\" rel=\"PrettyPhoto[342]\" style=\"border:0px; padding-top: 5px; float:left;\" alt=\"Share Button\"\/><\/a><script type=\"text\/javascript\">var hupso_services_t=new Array(\"Twitter\",\"Facebook\",\"Google Plus\");var hupso_background_t=\"#EAF4FF\";var hupso_border_t=\"#66CCFF\";var hupso_toolbar_size_t=\"big\";var hupso_image_folder_url = \"\";var hupso_url_t=\"\";var hupso_title_t=\"Maladie%20rare\";<\/script><script type=\"text\/javascript\" src=\"http:\/\/static.hupso.com\/share\/js\/share_toolbar.js\"><\/script><!-- Hupso Share Buttons --><\/div>","protected":false},"excerpt":{"rendered":"<p>Dystrophie maculaire h\u00e9r\u00e9ditaire la plus fr\u00e9quente La maladie de Stargardt est une maladie rare\u00a0d&rsquo;origine\u00a0g\u00e9n\u00e9tique. Elle repr\u00e9sente la dystrophie maculaire h\u00e9r\u00e9ditaire la plus fr\u00e9quente. Une maladie est dite rare quand elle touche moins d\u2019une personne sur 2\u00a0000, soit pour la France moins de 30 000 personnes pour une maladie. Elle concerne 1,2 personne pour 10\u00a0000. Pays&#8230;<\/p>\n<div style=\"padding-bottom:20px; padding-top:10px;\" class=\"hupso-share-buttons\"><!-- Hupso Share Buttons - https:\/\/www.hupso.com\/share\/ --><a class=\"hupso_toolbar\" href=\"https:\/\/www.hupso.com\/share\/\"><img src=\"http:\/\/static.hupso.com\/share\/buttons\/lang\/fr\/share.png\" style=\"border:0px; padding-top: 5px; float:left;\" alt=\"Share Button\"\/><\/a><script type=\"text\/javascript\">var hupso_services_t=new Array(\"Twitter\",\"Facebook\",\"Google Plus\");var hupso_background_t=\"#EAF4FF\";var hupso_border_t=\"#66CCFF\";var hupso_toolbar_size_t=\"big\";var hupso_image_folder_url = \"\";var hupso_url_t=\"\";var hupso_title_t=\"Maladie%20rare\";<\/script><script type=\"text\/javascript\" src=\"http:\/\/static.hupso.com\/share\/js\/share_toolbar.js\"><\/script><!-- Hupso Share Buttons --><\/div>","protected":false},"author":2,"featured_media":0,"parent":299,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v19.4 - 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